ICD-10: G93.2
Benign intracranial hypertension
Clinical Information
Inclusion Terms
- Pseudotumor
Additional Information
Description
Benign intracranial hypertension (BIH), classified under ICD-10-CM code G93.2, is a neurological condition characterized by increased intracranial pressure without an identifiable cause. This condition is often associated with symptoms that can significantly impact a patient's quality of life. Below is a detailed overview of the clinical description, symptoms, diagnosis, and management of BIH.
Clinical Description
Definition
Benign intracranial hypertension, also known as pseudotumor cerebri, is a condition where the pressure inside the skull rises without the presence of a tumor or other diseases that typically cause increased intracranial pressure. The term "benign" indicates that, while the condition can cause significant symptoms, it is not associated with a life-threatening underlying pathology.
Etiology
The exact cause of BIH is often unknown, but several factors have been associated with its development, including:
- Obesity: A significant number of patients with BIH are overweight or obese.
- Hormonal changes: Conditions such as pregnancy or the use of certain medications (e.g., corticosteroids, tetracycline) can contribute to the onset of BIH.
- Other medical conditions: Conditions like polycystic ovary syndrome (PCOS) and certain endocrine disorders may also play a role.
Symptoms
Patients with benign intracranial hypertension may experience a range of symptoms, including:
- Headaches: Often described as pulsating and can be severe.
- Visual disturbances: This may include blurred vision, double vision, or transient visual obscurations.
- Tinnitus: Ringing in the ears is a common complaint.
- Nausea and vomiting: These symptoms can occur due to increased intracranial pressure.
- Papilledema: Swelling of the optic nerve head, which can be observed during an eye examination.
Diagnosis
The diagnosis of BIH typically involves a combination of clinical evaluation and diagnostic imaging. Key steps include:
- Clinical history and physical examination: A thorough assessment of symptoms and medical history is essential.
- Neuroimaging: MRI or CT scans are performed to rule out other causes of increased intracranial pressure, such as tumors or structural abnormalities.
- Lumbar puncture: Measuring the cerebrospinal fluid (CSF) pressure can confirm elevated intracranial pressure and help in the diagnosis.
Management
Management of benign intracranial hypertension focuses on alleviating symptoms and preventing complications, particularly vision loss. Treatment options may include:
- Weight management: For overweight patients, weight loss can significantly reduce symptoms and intracranial pressure.
- Medications: Acetazolamide is commonly prescribed to decrease CSF production. Other medications may include corticosteroids or diuretics.
- Surgical interventions: In cases where medical management is insufficient, procedures such as optic nerve sheath fenestration or shunt placement may be considered to relieve pressure.
Conclusion
Benign intracranial hypertension is a manageable condition, but it requires careful diagnosis and treatment to prevent complications, particularly regarding vision. Awareness of the symptoms and risk factors is crucial for early detection and intervention. Regular follow-up with healthcare providers is essential to monitor the condition and adjust treatment as necessary. For further information or specific case management, consulting a neurologist or a specialist in headache medicine may be beneficial.
Clinical Information
Benign intracranial hypertension (BIH), classified under ICD-10 code G93.2, is a condition characterized by increased intracranial pressure without an identifiable cause. This condition is often seen in specific patient populations and presents with a range of clinical signs and symptoms. Below, we explore the clinical presentation, signs, symptoms, and patient characteristics associated with BIH.
Clinical Presentation
Definition and Overview
Benign intracranial hypertension, also known as idiopathic intracranial hypertension (IIH), is defined by elevated cerebrospinal fluid (CSF) pressure, typically greater than 25 cm H2O, in the absence of a mass lesion or other identifiable causes of increased intracranial pressure. It is crucial to differentiate BIH from secondary causes of increased intracranial pressure, such as tumors or infections, which require different management strategies[1][2].
Common Symptoms
Patients with BIH often present with a variety of symptoms, which can significantly impact their quality of life. The most common symptoms include:
- Headaches: These are often described as pulsatile and can be severe, resembling migraines. They may worsen with activities such as bending over or straining[3].
- Visual Disturbances: Patients may experience transient visual obscurations, blurred vision, or even permanent vision loss due to optic nerve damage (papilledema) if left untreated[4].
- Tinnitus: A ringing or buzzing sound in the ears is frequently reported, which can be distressing for patients[5].
- Nausea and Vomiting: These symptoms may occur, particularly during episodes of severe headache[6].
Signs on Examination
During a clinical examination, several signs may be observed:
- Papilledema: Swelling of the optic disc is a hallmark sign of increased intracranial pressure and can be detected during a fundoscopic examination[7].
- Visual Field Defects: Testing may reveal defects, particularly in the peripheral vision, due to optic nerve compression[8].
- Neurological Examination: Most patients will have a normal neurological examination aside from the signs related to increased intracranial pressure[9].
Patient Characteristics
Demographics
Certain demographic factors are associated with a higher incidence of BIH:
- Gender: BIH is more prevalent in women, particularly those of childbearing age. The female-to-male ratio is approximately 3:1[10].
- Obesity: A significant risk factor for BIH is obesity, with many patients having a body mass index (BMI) greater than 30. Weight gain is often noted prior to the onset of symptoms[11].
- Age: While BIH can occur at any age, it is most commonly diagnosed in young to middle-aged adults, particularly women aged 20 to 50 years[12].
Associated Conditions
Patients with BIH may also have comorbid conditions that can influence the presentation and management of the disease:
- Polycystic Ovary Syndrome (PCOS): There is a noted association between BIH and PCOS, which may contribute to the higher prevalence in women[13].
- Medications: Certain medications, such as tetracyclines and corticosteroids, have been implicated in the development of BIH[14].
Conclusion
Benign intracranial hypertension is a complex condition characterized by increased intracranial pressure without an identifiable cause. Its clinical presentation includes severe headaches, visual disturbances, and signs of papilledema. The condition predominantly affects young, obese women, and understanding these characteristics is crucial for timely diagnosis and management. Early intervention is essential to prevent complications, particularly vision loss, making awareness of the signs and symptoms vital for healthcare providers.
Approximate Synonyms
Benign intracranial hypertension (BIH), classified under ICD-10 code G93.2, is a condition characterized by increased intracranial pressure without an identifiable cause. This condition is also known by several alternative names and related terms, which can help in understanding its clinical context and implications.
Alternative Names for Benign Intracranial Hypertension
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Idiopathic Intracranial Hypertension (IIH): This is perhaps the most common alternative name for benign intracranial hypertension. The term "idiopathic" indicates that the exact cause of the increased pressure is unknown, which is a hallmark of this condition[6][15].
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Pseudotumor Cerebri: This term translates to "false brain tumor" and reflects the condition's symptoms, which can mimic those of a brain tumor, such as headaches and visual disturbances, despite the absence of a tumor[15].
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Benign Intracranial Hypertension Syndrome: This term emphasizes the syndrome aspect of the condition, highlighting the collection of symptoms associated with increased intracranial pressure[12].
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Venous Sinus Thrombosis: While not synonymous, this term is related as it can be a cause of secondary intracranial hypertension. It refers to the formation of a blood clot in the brain's venous sinuses, which can lead to increased pressure[5].
Related Terms and Concepts
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Increased Intracranial Pressure (ICP): This is a broader term that encompasses any condition where the pressure inside the skull is elevated, including benign intracranial hypertension[15].
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Cerebral Venous Insufficiency: This term refers to inadequate blood flow from the brain, which can contribute to increased intracranial pressure and is sometimes associated with BIH[5].
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Obesity: While not a term for BIH itself, obesity is a significant risk factor for developing idiopathic intracranial hypertension, and discussions around BIH often include this term due to its prevalence in affected populations[6][15].
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Visual Disturbances: This term is often used in clinical discussions regarding BIH, as one of the common symptoms includes changes in vision, which can be a critical aspect of diagnosis and management[15].
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Headaches: Similar to visual disturbances, headaches are a primary symptom of benign intracranial hypertension and are frequently mentioned in relation to the condition[15].
Conclusion
Understanding the alternative names and related terms for ICD-10 code G93.2 is essential for healthcare professionals and patients alike. These terms not only aid in accurate diagnosis and treatment but also enhance communication regarding the condition. If you have further questions about benign intracranial hypertension or its management, feel free to ask!
Diagnostic Criteria
Benign intracranial hypertension (BIH), also known as idiopathic intracranial hypertension (IIH), is a condition characterized by increased intracranial pressure without an identifiable cause. The diagnosis of BIH is guided by specific clinical criteria and diagnostic tests. Below, we outline the key criteria and considerations used in diagnosing this condition, particularly in relation to the ICD-10 code G93.2.
Clinical Criteria for Diagnosis
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Symptoms: Patients typically present with symptoms such as:
- Headaches, often described as pulsatile or similar to migraines.
- Visual disturbances, including transient visual obscurations or permanent vision loss.
- Tinnitus, particularly a ringing sound that may be synchronous with the heartbeat (pulsatile tinnitus).
- Nausea and vomiting may also occur. -
Neurological Examination: A thorough neurological examination is essential to rule out other causes of increased intracranial pressure. This includes assessing:
- Visual acuity and visual fields.
- Fundoscopic examination to check for papilledema (swelling of the optic nerve head). -
Imaging Studies: Neuroimaging is crucial to exclude secondary causes of increased intracranial pressure. Common imaging modalities include:
- Magnetic Resonance Imaging (MRI): This helps to identify any structural abnormalities, such as tumors or venous sinus thrombosis.
- Computed Tomography (CT): A CT scan can also be used to rule out other intracranial pathologies. -
Lumbar Puncture: A lumbar puncture (spinal tap) is often performed to measure cerebrospinal fluid (CSF) pressure. Key points include:
- Elevated opening pressure (typically >250 mm H2O).
- Normal CSF composition (no signs of infection or other abnormalities). -
Exclusion of Secondary Causes: It is essential to rule out secondary causes of intracranial hypertension, such as:
- Obesity, which is a significant risk factor for BIH.
- Medications (e.g., tetracyclines, corticosteroids).
- Endocrine disorders (e.g., Cushing's syndrome).
Additional Considerations
- Diagnostic Criteria: The modified Dandy criteria are often used for diagnosing IIH, which include:
- Symptoms of increased intracranial pressure.
- Evidence of papilledema.
- Normal neurological examination (except for visual field defects).
- Normal neuroimaging.
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Elevated CSF pressure with normal CSF composition.
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Risk Factors: Certain populations are at higher risk for BIH, including overweight women of childbearing age. Understanding these demographics can aid in diagnosis and management.
Conclusion
The diagnosis of benign intracranial hypertension (ICD-10 code G93.2) relies on a combination of clinical symptoms, neurological examination, imaging studies, and lumbar puncture results. By systematically ruling out secondary causes and confirming elevated intracranial pressure with normal CSF analysis, healthcare providers can accurately diagnose this condition and initiate appropriate management strategies. If you suspect BIH, it is crucial to consult a healthcare professional for a comprehensive evaluation and diagnosis.
Treatment Guidelines
Benign intracranial hypertension (BIH), also known as idiopathic intracranial hypertension (IIH), is characterized by increased intracranial pressure without an identifiable cause. The ICD-10 code for this condition is G93.2. The management of BIH focuses on alleviating symptoms, reducing intracranial pressure, and preventing complications. Here’s a detailed overview of standard treatment approaches for this condition.
Diagnosis and Initial Assessment
Before treatment can begin, a thorough diagnostic process is essential. This typically includes:
- Clinical Evaluation: A detailed history and physical examination to assess symptoms such as headaches, visual disturbances, and signs of increased intracranial pressure.
- Neuroimaging: MRI or CT scans are performed to rule out secondary causes of increased intracranial pressure, such as tumors or venous sinus thrombosis.
- Lumbar Puncture: Measuring the opening pressure during a lumbar puncture can confirm elevated intracranial pressure and allow for cerebrospinal fluid (CSF) analysis.
Standard Treatment Approaches
1. Medical Management
- Weight Management: For overweight patients, weight loss is often the first-line recommendation, as it has been shown to significantly reduce symptoms and intracranial pressure[1].
- Medications:
- Acetazolamide: This carbonic anhydrase inhibitor is commonly prescribed to reduce CSF production and lower intracranial pressure. Dosages typically range from 500 mg to 2000 mg per day, depending on the patient's tolerance and response[2].
- Topiramate: Another medication that may be used for its weight loss effects and ability to reduce intracranial pressure[3].
- Diuretics: In some cases, diuretics like furosemide may be used to help manage fluid balance and reduce pressure[4].
2. Surgical Interventions
When medical management fails to alleviate symptoms or if there is a risk of vision loss, surgical options may be considered:
- Optic Nerve Sheath Fenestration: This procedure involves creating a small opening in the sheath surrounding the optic nerve to relieve pressure and prevent vision loss[5].
- CSF Shunt Placement: Ventriculoperitoneal shunts or lumboperitoneal shunts can be placed to divert excess CSF and reduce intracranial pressure. This is often reserved for more severe cases or when other treatments have not been effective[6].
3. Monitoring and Follow-Up
Regular follow-up appointments are crucial for monitoring the condition and adjusting treatment as necessary. This may include:
- Visual Field Testing: To assess any changes in vision and detect early signs of optic nerve damage.
- Regular Imaging: Periodic MRI or CT scans may be performed to monitor for any changes in intracranial structures or the development of complications.
Conclusion
The management of benign intracranial hypertension (ICD-10 code G93.2) involves a combination of lifestyle modifications, medical therapy, and potentially surgical interventions, depending on the severity of the condition and the patient's response to initial treatments. Weight loss and medications like acetazolamide are foundational in treatment, while surgical options are available for those with more severe symptoms or complications. Ongoing monitoring is essential to ensure effective management and to prevent long-term complications, particularly regarding vision.
For patients experiencing symptoms of BIH, early diagnosis and intervention are key to improving outcomes and quality of life.
Related Information
Description
- Increased intracranial pressure without cause
- Symptoms impact quality of life
- No identifiable underlying pathology
- Obesity and hormonal changes contribute to BIH
- Headaches, visual disturbances, tinnitus common symptoms
- Papilledema is a characteristic sign
- Diagnosis involves clinical evaluation and imaging
- Treatment focuses on alleviating symptoms and preventing complications
Clinical Information
- Increased intracranial pressure without identifiable cause
- Typically >25 cm H2O cerebrospinal fluid pressure
- Pulsatile headaches often severe and worsen with activities
- Transient visual obscurations, blurred vision or permanent loss
- Ringing or buzzing sound in the ears (tinnitus)
- Nausea and vomiting during episodes of headache
- Swelling of optic disc (papilledema) detectable by fundoscopy
- Visual field defects particularly peripheral vision
- Normal neurological examination aside from increased intracranial pressure signs
- More prevalent in women especially childbearing age 3:1 ratio
- Obesity is a significant risk factor BMI >30
- Commonly diagnosed in young to middle-aged adults aged 20-50 years
- Associated with Polycystic Ovary Syndrome (PCOS)
- Certain medications like tetracyclines and corticosteroids implicated
Approximate Synonyms
- Idiopathic Intracranial Hypertension
- Pseudotumor Cerebri
- Benign Intracranial Hypertension Syndrome
- Increased Intracranial Pressure
- Cerebral Venous Insufficiency
- Obesity
- Visual Disturbances
- Headaches
Diagnostic Criteria
- Headaches are typically pulsatile or migrainous
- Visual disturbances with transient obscurations or loss
- Tinnitus synchronous with heartbeat (pulsatile)
- Nausea and vomiting may occur
- Normal CSF composition despite elevated pressure
- Papilledema on fundoscopic examination
- Elevated opening pressure >250 mm H2O
- Normal neurological exam except for visual field defects
Treatment Guidelines
- Weight loss for overweight patients
- Acetazolamide medication reduces CSF production
- Topiramate for weight loss and pressure reduction
- Diuretics manage fluid balance and pressure
- Optic Nerve Sheath Fenestration for pressure relief
- CSF Shunt Placement for severe cases or complications
- Regular visual field testing monitors vision changes
Coding Guidelines
Excludes 1
- hypertensive encephalopathy (I67.4)
- obstructive hydrocephalus (G91.1)
Related Diseases
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