ICD-10: H47.143
Foster-Kennedy syndrome, bilateral
Additional Information
Diagnostic Criteria
Foster-Kennedy syndrome is a rare neurological condition characterized by a specific set of symptoms, primarily involving optic nerve atrophy and the presence of a tumor, often affecting the frontal lobe. The diagnosis of Foster-Kennedy syndrome, particularly when coded under ICD-10 code H47.143 (which refers to bilateral papilledema), involves several clinical criteria and diagnostic evaluations.
Clinical Criteria for Diagnosis
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Optic Nerve Atrophy: The presence of bilateral optic nerve atrophy is a hallmark of Foster-Kennedy syndrome. This can be assessed through a comprehensive eye examination, including visual acuity tests and fundoscopic examination, which may reveal pale optic discs.
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Papilledema: Bilateral papilledema, indicated by the ICD-10 code H47.143, is a critical feature. This condition is characterized by swelling of the optic disc due to increased intracranial pressure. It can be evaluated through direct observation during an eye examination.
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Neurological Symptoms: Patients may present with various neurological symptoms, including:
- Headaches
- Visual disturbances (e.g., blurred vision, loss of peripheral vision)
- Cognitive changes or personality alterations, which may arise from frontal lobe involvement. -
Imaging Studies: Neuroimaging, such as MRI or CT scans, is essential to identify any underlying mass lesions, particularly tumors in the frontal lobe that could be causing the symptoms. The imaging should show evidence of a mass effect or displacement of the optic nerves.
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Exclusion of Other Conditions: It is crucial to rule out other causes of optic nerve atrophy and papilledema, such as other types of intracranial tumors, inflammatory conditions, or vascular issues. This may involve additional tests, including blood tests and lumbar puncture if necessary.
Diagnostic Process
- History and Physical Examination: A thorough medical history and neurological examination are vital to assess the presence of symptoms associated with Foster-Kennedy syndrome.
- Visual Field Testing: This can help determine the extent of visual impairment and any specific patterns of vision loss associated with optic nerve damage.
- Referral to Specialists: In many cases, referral to a neurologist or ophthalmologist may be necessary for further evaluation and management.
Conclusion
The diagnosis of Foster-Kennedy syndrome under ICD-10 code H47.143 requires a combination of clinical findings, imaging studies, and the exclusion of other potential causes of the symptoms. The presence of bilateral optic nerve atrophy and papilledema, along with neurological symptoms and imaging evidence of a frontal lobe mass, are critical components in establishing this diagnosis. Proper identification and management are essential to address the underlying causes and mitigate the impact on the patient's vision and overall health.
Clinical Information
Foster-Kennedy syndrome is a rare neurological condition characterized by a specific set of clinical presentations, signs, and symptoms. It is primarily associated with increased intracranial pressure and optic nerve dysfunction, often resulting from a mass lesion, such as a tumor, affecting the frontal lobe. Below is a detailed overview of the clinical presentation, signs, symptoms, and patient characteristics associated with ICD-10 code H47.143, which pertains to bilateral Foster-Kennedy syndrome.
Clinical Presentation
Foster-Kennedy syndrome typically manifests in adults, although it can occur in children. The syndrome is characterized by a combination of visual disturbances and neurological deficits due to the effects of a mass lesion on the optic nerves and surrounding structures. The most common underlying cause is a frontal lobe tumor, such as a meningioma, which can lead to increased intracranial pressure.
Signs and Symptoms
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Visual Impairment:
- Bilateral Optic Atrophy: Patients often present with bilateral optic nerve atrophy, which can be observed during an eye examination. This atrophy is a result of chronic pressure on the optic nerves.
- Visual Field Defects: Patients may experience specific visual field deficits, such as bitemporal hemianopsia, due to the involvement of the optic chiasm. -
Papilledema:
- Swelling of the Optic Nerve Head: Papilledema is commonly observed in patients with Foster-Kennedy syndrome, indicating increased intracranial pressure. This can lead to further visual disturbances if not addressed. -
Neurological Symptoms:
- Headaches: Patients frequently report persistent headaches, which may be exacerbated by changes in position or straining.
- Cognitive Changes: Depending on the extent of the mass effect, cognitive impairments, personality changes, or other neurological deficits may occur. -
Other Symptoms:
- Nausea and Vomiting: These symptoms can arise from increased intracranial pressure.
- Seizures: In some cases, seizures may occur, particularly if the mass lesion irritates the surrounding brain tissue.
Patient Characteristics
- Age: Foster-Kennedy syndrome is more commonly diagnosed in adults, particularly in middle-aged individuals, although it can occur in younger patients.
- Gender: There is no strong gender predilection, but some studies suggest a slight male predominance.
- Underlying Conditions: Patients may have a history of other neurological conditions or risk factors for intracranial tumors, such as previous radiation therapy or genetic predispositions.
Conclusion
Foster-Kennedy syndrome, classified under ICD-10 code H47.143, presents with a distinct combination of visual and neurological symptoms primarily due to the effects of a mass lesion in the frontal lobe. Early recognition of the signs, such as bilateral optic atrophy and papilledema, is crucial for timely intervention and management. Given the potential for significant morbidity associated with untreated intracranial pressure, a thorough clinical evaluation and imaging studies are essential for diagnosis and treatment planning.
Description
Foster-Kennedy syndrome is a rare neurological condition characterized by a specific set of clinical features primarily affecting the optic nerves and the surrounding structures. The ICD-10 code H47.143 specifically refers to the bilateral presentation of this syndrome. Below is a detailed overview of the clinical description, symptoms, and relevant details associated with Foster-Kennedy syndrome.
Clinical Description of Foster-Kennedy Syndrome
Foster-Kennedy syndrome is typically associated with increased intracranial pressure, often due to a mass lesion, such as a tumor, located in the frontal lobe. The syndrome is characterized by the following key features:
Key Symptoms
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Optic Atrophy: This is a hallmark of Foster-Kennedy syndrome, where there is degeneration of the optic nerve, leading to vision loss. In bilateral cases, both optic nerves are affected, resulting in significant visual impairment.
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Papilledema: The condition often presents with swelling of the optic disc (papilledema) due to increased intracranial pressure. This can be observed during a fundoscopic examination.
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Loss of Sense of Smell (Anosmia): Patients may experience a loss of the sense of smell, which can be attributed to the involvement of the olfactory nerve or the frontal lobe.
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Visual Field Defects: Patients may exhibit specific visual field deficits, which can vary depending on the extent and location of the optic nerve involvement.
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Headaches: Many patients report headaches, which are often a result of the underlying increased intracranial pressure.
Etiology
Foster-Kennedy syndrome is most commonly associated with frontal lobe tumors, particularly meningiomas. These tumors can exert pressure on the optic nerves and surrounding structures, leading to the characteristic symptoms of the syndrome. Other potential causes may include traumatic brain injury or other intracranial lesions that result in similar clinical presentations.
Diagnosis
Diagnosis of Foster-Kennedy syndrome typically involves a combination of clinical evaluation and imaging studies. Key diagnostic steps include:
- Neurological Examination: A thorough neurological assessment to evaluate visual acuity, visual fields, and signs of increased intracranial pressure.
- Imaging Studies: MRI or CT scans of the brain are crucial for identifying any mass lesions in the frontal lobe that may be causing the symptoms.
Management
Management of Foster-Kennedy syndrome focuses on addressing the underlying cause, particularly if a tumor is present. Treatment options may include:
- Surgical Intervention: If a mass lesion is identified, surgical removal may be necessary to alleviate pressure on the optic nerves and surrounding structures.
- Medical Management: In cases where surgery is not immediately indicated, corticosteroids may be used to reduce inflammation and intracranial pressure.
Conclusion
Foster-Kennedy syndrome, particularly in its bilateral form (ICD-10 code H47.143), presents a unique set of challenges due to its association with optic nerve atrophy and increased intracranial pressure. Early diagnosis and intervention are critical to managing the condition effectively and preserving vision. Understanding the clinical features and underlying causes is essential for healthcare providers in order to provide appropriate care and treatment for affected patients.
Approximate Synonyms
Foster-Kennedy syndrome, classified under ICD-10 code H47.143, is a rare neurological condition characterized by specific clinical features. Understanding its alternative names and related terms can enhance clarity in medical documentation and communication. Below is a detailed overview of the alternative names and related terms associated with this syndrome.
Alternative Names for Foster-Kennedy Syndrome
- Foster-Kennedy Syndrome: The primary name used in medical literature.
- Bilateral Foster-Kennedy Syndrome: This term emphasizes the bilateral nature of the condition, which is relevant for coding and diagnosis.
- Optic Atrophy with Papilledema: This description highlights two key features of the syndrome—optic nerve damage (atrophy) and swelling of the optic disc (papilledema).
- Papilledema with Contralateral Optic Atrophy: This term describes the syndrome's hallmark signs, where one eye exhibits swelling while the other shows optic nerve atrophy.
Related Terms
- Optic Nerve Atrophy: A condition where the optic nerve is damaged, leading to vision loss, which is a significant aspect of Foster-Kennedy syndrome.
- Intracranial Hypertension: Often associated with Foster-Kennedy syndrome, this condition involves increased pressure within the skull, which can lead to papilledema.
- Visual Field Defects: Patients may experience specific patterns of vision loss, which are important for diagnosis and management.
- Neurological Deficits: General term referring to impairments in the nervous system that may accompany Foster-Kennedy syndrome.
Clinical Context
Foster-Kennedy syndrome is typically associated with conditions that cause increased intracranial pressure, such as tumors or other mass lesions. The syndrome is characterized by the presence of papilledema in one eye and optic atrophy in the contralateral eye, which can complicate diagnosis and treatment strategies.
Understanding these alternative names and related terms is crucial for healthcare professionals involved in the diagnosis, treatment, and coding of this syndrome. Accurate terminology ensures effective communication among medical teams and aids in the proper documentation for billing and coding purposes.
In summary, recognizing the various names and related terms for Foster-Kennedy syndrome can facilitate better understanding and management of this complex condition, ultimately leading to improved patient outcomes.
Treatment Guidelines
Foster-Kennedy syndrome (FKS) is a rare neurological condition characterized by a combination of symptoms resulting from increased intracranial pressure, often due to a mass lesion affecting the optic nerve. The ICD-10 code for bilateral Foster-Kennedy syndrome is H47.143. Understanding the standard treatment approaches for this condition is crucial for effective management and patient care.
Overview of Foster-Kennedy Syndrome
Foster-Kennedy syndrome typically presents with the following symptoms:
- Bilateral optic atrophy: This occurs due to damage to the optic nerve.
- Papilledema: Swelling of the optic disc due to increased intracranial pressure.
- Loss of vision: Patients may experience varying degrees of visual impairment.
- Other neurological deficits: Depending on the underlying cause, patients may exhibit additional neurological symptoms.
The most common underlying cause of Foster-Kennedy syndrome is a tumor, such as a meningioma, located in the anterior cranial fossa, which exerts pressure on the optic nerves.
Standard Treatment Approaches
1. Surgical Intervention
Surgery is often the primary treatment for Foster-Kennedy syndrome, especially when a mass lesion is identified. The goals of surgical intervention include:
- Tumor removal: If a tumor is the cause, resection can alleviate pressure on the optic nerves and potentially restore vision.
- Decompression: In cases where the tumor cannot be completely removed, decompression of the optic nerve may be performed to relieve pressure.
2. Medical Management
In addition to surgical options, medical management plays a crucial role in treating Foster-Kennedy syndrome:
- Corticosteroids: These may be prescribed to reduce inflammation and edema around the optic nerve, particularly if there is associated swelling.
- Diuretics: Medications such as acetazolamide can help decrease intracranial pressure by promoting fluid excretion.
- Pain management: Analgesics may be necessary to manage headaches or discomfort associated with increased intracranial pressure.
3. Monitoring and Follow-Up
Regular monitoring is essential for patients with Foster-Kennedy syndrome:
- Visual field testing: This helps assess the extent of vision loss and monitor any changes over time.
- Neuroimaging: MRI or CT scans are used to track the status of any identified lesions and assess for recurrence post-surgery.
4. Rehabilitation Services
For patients experiencing significant vision loss, rehabilitation services can be beneficial:
- Vision therapy: Tailored programs can help patients adapt to changes in vision.
- Occupational therapy: This can assist patients in managing daily activities and improving quality of life.
Conclusion
The management of Foster-Kennedy syndrome requires a multidisciplinary approach, combining surgical, medical, and rehabilitative strategies to address the complex needs of patients. Early diagnosis and intervention are critical to improving outcomes, particularly in preserving vision and alleviating symptoms associated with increased intracranial pressure. Regular follow-up and monitoring are essential to ensure ongoing care and address any complications that may arise.
Related Information
Diagnostic Criteria
- Bilateral optic nerve atrophy present
- Papilledema with bilateral swelling observed
- Neurological symptoms including headaches and visual disturbances
- Imaging studies show mass lesions in frontal lobe
- Exclusion of other conditions such as tumors or inflammation
Clinical Information
- Bilateral Optic Atrophy
- Visual Field Defects Occur
- Papilledema Commonly Observed
- Headaches Persistent and Exacerbated
- Cognitive Changes Can Occur
- Nausea and Vomiting Possible
- Seizures Can Occur in Some
Description
Approximate Synonyms
Treatment Guidelines
- Surgical Intervention: Tumor removal
- Decompression of optic nerve
- Corticosteroids for inflammation reduction
- Diuretics for intracranial pressure management
- Pain management with analgesics
- Regular visual field testing
- Neuroimaging monitoring post-surgery
Related Diseases
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