ICD-10: Q71.63

Lobster-claw hand, bilateral

Additional Information

Description

Lobster-claw hand, bilateral, is classified under the ICD-10-CM code Q71.63. This condition is a congenital malformation characterized by a specific deformity of the hands, resembling the claws of a lobster. Below is a detailed clinical description and relevant information regarding this diagnosis.

Clinical Description

Definition

Lobster-claw hand, also known as symbrachydactyly, is a congenital condition where the hand is malformed, typically resulting in a reduced number of fingers or a fusion of fingers. In bilateral cases, both hands are affected, leading to significant functional limitations.

Characteristics

  • Appearance: The hands may appear claw-like, with a significant reduction in the length of the fingers. The thumb may be absent or underdeveloped, and the remaining fingers may be fused or have limited mobility.
  • Functionality: Individuals with lobster-claw hand often experience challenges with grip and fine motor skills, which can impact daily activities and overall quality of life.
  • Associated Conditions: This condition can occur as part of syndromes or may be isolated. It is often associated with other congenital anomalies, particularly those affecting the upper limbs.

Diagnosis

The diagnosis of lobster-claw hand is typically made through clinical examination and may be confirmed with imaging studies to assess the structure of the bones and soft tissues in the hands. Genetic counseling may also be recommended, especially if there is a family history of congenital malformations.

Treatment Options

Treatment for lobster-claw hand is multidisciplinary and may include:
- Surgical Intervention: Surgical procedures may be performed to improve hand function, such as reconstructive surgery to separate fused fingers or to create a more functional thumb.
- Occupational Therapy: Therapy can help individuals develop adaptive strategies to enhance their daily living skills and improve hand function.
- Prosthetics: In some cases, prosthetic devices may be considered to assist with functionality.

Coding and Billing

The ICD-10-CM code Q71.63 is a billable code used for insurance and medical billing purposes. It is essential for healthcare providers to accurately document this diagnosis to ensure appropriate reimbursement for treatment and services rendered.

Conclusion

Lobster-claw hand, bilateral, is a significant congenital condition that affects hand morphology and functionality. Early diagnosis and a comprehensive treatment plan involving surgical and therapeutic interventions can greatly enhance the quality of life for affected individuals. Understanding the clinical implications and management strategies is crucial for healthcare providers working with patients diagnosed with this condition.

Clinical Information

Lobster-claw hand, also known as bilateral lobster-claw hand, is a congenital malformation characterized by specific deformities of the hands. This condition is classified under the ICD-10-CM code Q71.63. Below is a detailed overview of its clinical presentation, signs, symptoms, and patient characteristics.

Clinical Presentation

Lobster-claw hand is primarily recognized by its distinctive appearance, which resembles the claws of a lobster. This condition typically involves:

  • Hypoplasia of the central digits: The second and third fingers are often underdeveloped or absent, leading to a claw-like appearance.
  • Prominent thumb and little finger: The thumb and little finger may be more pronounced, contributing to the characteristic shape.
  • Possible syndactyly: In some cases, there may be fusion of the fingers (syndactyly), which can further complicate the hand's appearance and function.

Signs and Symptoms

Patients with bilateral lobster-claw hand may exhibit a range of signs and symptoms, including:

  • Deformity of the hands: The most noticeable sign is the abnormal shape of the hands, which can affect the patient's ability to grasp or manipulate objects.
  • Functional limitations: Depending on the severity of the malformation, individuals may experience difficulties with fine motor skills, impacting daily activities such as writing or buttoning clothing.
  • Associated conditions: Lobster-claw hand can occur as part of syndromes such as Holt-Oram syndrome or other congenital anomalies, which may present additional health challenges.

Patient Characteristics

The characteristics of patients with bilateral lobster-claw hand can vary widely, but some common aspects include:

  • Congenital origin: This condition is present at birth and is classified as a congenital malformation.
  • Family history: There may be a genetic component, as congenital hand deformities can run in families.
  • Demographics: While lobster-claw hand can affect individuals of any gender or ethnicity, some studies suggest a slight male predominance in congenital hand deformities.

Conclusion

Bilateral lobster-claw hand (ICD-10 code Q71.63) is a congenital condition marked by distinctive hand deformities that can significantly impact an individual's functionality and quality of life. Early diagnosis and intervention, including potential surgical correction and occupational therapy, can help improve hand function and overall outcomes for affected individuals. Understanding the clinical presentation, signs, symptoms, and patient characteristics is crucial for healthcare providers in managing this condition effectively.

Approximate Synonyms

The ICD-10-CM code Q71.63 refers specifically to "Lobster-claw hand, bilateral," a congenital condition characterized by a distinctive hand deformity. This condition is often associated with various syndromes and can be described using alternative names and related terms. Below is a detailed overview of these terms.

Alternative Names for Lobster-Claw Hand

  1. Ectrodactyly: This is the most common term used to describe the condition, which refers to the absence of one or more central digits of the hand or foot, leading to a claw-like appearance.

  2. Split Hand/Foot Malformation (SHFM): This term encompasses a broader category of congenital malformations that include lobster-claw hand as a specific manifestation.

  3. Cleft Hand: While this term can refer to various forms of hand deformities, it is sometimes used interchangeably with lobster-claw hand, particularly when describing the cleft-like appearance of the hand.

  4. Lobster Claw Deformity: This is a descriptive term that emphasizes the resemblance of the hand to a lobster's claw, highlighting the characteristic shape.

  1. Congenital Limb Deformities: This broader category includes various congenital conditions affecting limb formation, of which lobster-claw hand is a specific type.

  2. Syndromes Associated with Ectrodactyly:
    - Ectrodactyly-Ectodermal Dysplasia-Clefting (EEC) Syndrome: A genetic condition that includes lobster-claw hand as one of its features.
    - Split Hand/Foot Malformation (SHFM) Syndromes: A group of genetic disorders that can present with lobster-claw hand.

  3. Genetic Mutations: Specific genetic mutations, such as those in the TP63 gene, are often associated with ectrodactyly and related syndromes.

  4. Congenital Anomalies: This term refers to a wide range of birth defects, including those affecting the hands and feet, and encompasses conditions like lobster-claw hand.

Conclusion

Understanding the alternative names and related terms for ICD-10 code Q71.63 is essential for accurate diagnosis, coding, and communication among healthcare professionals. The terms "ectrodactyly," "split hand/foot malformation," and "cleft hand" are particularly significant, as they provide insight into the nature of the condition and its potential associations with genetic syndromes. If further information or clarification is needed regarding specific aspects of this condition, please feel free to ask.

Diagnostic Criteria

Lobster-claw hand, classified under ICD-10 code Q71.63, refers to a specific congenital malformation characterized by a distinctive hand deformity. This condition is part of a broader category of congenital malformations, deformations, and chromosomal abnormalities. To diagnose this condition accurately, healthcare professionals typically rely on a combination of clinical evaluation, patient history, and specific diagnostic criteria.

Diagnostic Criteria for Lobster-Claw Hand

Clinical Features

  1. Physical Examination: The primary method for diagnosing lobster-claw hand involves a thorough physical examination of the hands. Clinicians look for:
    - Deformity of the hand: The hand appears claw-like, with a significant reduction in the number of fingers or fusion of fingers (syndactyly).
    - Bilateral Presentation: In the case of Q71.63, the condition is bilateral, meaning it affects both hands symmetrically.

  2. Associated Anomalies: Lobster-claw hand may be associated with other congenital anomalies, which can aid in diagnosis. These may include:
    - Limb malformations
    - Other skeletal abnormalities
    - Possible syndromic associations, such as those seen in conditions like Holt-Oram syndrome or other genetic syndromes.

Diagnostic Imaging

  • X-rays: Radiographic imaging may be utilized to assess the bone structure of the hands and identify any underlying skeletal abnormalities that accompany the deformity.

Genetic Testing

  • Chromosomal Analysis: In some cases, genetic testing may be recommended to rule out or confirm associated syndromes, especially if there is a family history of congenital malformations.

Family and Medical History

  • Patient History: Gathering a comprehensive medical and family history is crucial. This includes:
  • Any known genetic conditions in the family.
  • Maternal health during pregnancy, including exposure to teratogens or infections.

Conclusion

The diagnosis of lobster-claw hand (ICD-10 code Q71.63) is primarily based on clinical evaluation, supported by imaging and genetic testing when necessary. The bilateral nature of the condition, along with its characteristic physical features, plays a significant role in establishing the diagnosis. Early identification and intervention are essential for managing the condition and improving functional outcomes for affected individuals. If you have further questions or need more specific information, feel free to ask!

Treatment Guidelines

Lobster-claw hand, classified under ICD-10 code Q71.63, refers to a congenital condition characterized by a specific malformation of the hands, where the fingers are fused or have a claw-like appearance. This condition can significantly impact hand function and aesthetics, necessitating a comprehensive treatment approach. Below, we explore standard treatment strategies for managing bilateral lobster-claw hand.

Overview of Lobster-Claw Hand

Lobster-claw hand is often associated with syndromes such as Apert syndrome or other congenital limb malformations. The condition can vary in severity, affecting the range of motion, grip strength, and overall functionality of the hands. Treatment typically involves a multidisciplinary approach, including surgical intervention, physical therapy, and occupational therapy.

Standard Treatment Approaches

1. Surgical Intervention

Surgery is often the primary treatment for lobster-claw hand, especially in cases where the malformation significantly impairs function. Surgical options may include:

  • Release Surgery: This involves separating fused fingers to improve mobility and function. The timing of surgery is crucial; it is often performed in early childhood to maximize developmental outcomes.
  • Reconstruction: In more severe cases, reconstructive surgery may be necessary to create a more functional hand structure. This can involve bone grafting or the use of prosthetic materials to enhance hand shape and function.
  • Tendon Transfers: If the muscles and tendons are affected, tendon transfer procedures may be performed to improve grip and dexterity.

2. Physical Therapy

Post-surgical rehabilitation is essential for restoring function and strength. Physical therapy may include:

  • Range of Motion Exercises: These exercises help maintain and improve flexibility in the fingers and wrists.
  • Strengthening Exercises: Targeted exercises can enhance muscle strength, which is crucial for hand function.
  • Adaptive Techniques: Therapists may teach patients how to perform daily activities using adaptive techniques to compensate for any limitations.

3. Occupational Therapy

Occupational therapy focuses on helping individuals achieve independence in daily activities. Key components include:

  • Skill Development: Therapists work with patients to develop fine motor skills necessary for tasks such as writing, buttoning clothes, and using utensils.
  • Assistive Devices: The use of splints or custom-made orthotics can support hand function and improve grip.
  • Environmental Modifications: Occupational therapists may recommend modifications to the home or workplace to facilitate easier access and usability.

4. Psychosocial Support

Living with a congenital hand condition can have psychological impacts. Providing support through counseling or support groups can help individuals cope with the emotional aspects of their condition. This is particularly important for children and adolescents as they navigate social interactions and self-image.

Conclusion

The treatment of bilateral lobster-claw hand (ICD-10 code Q71.63) is multifaceted, involving surgical, therapeutic, and psychosocial strategies to optimize hand function and quality of life. Early intervention is critical to achieving the best outcomes, and a collaborative approach among healthcare providers, patients, and families is essential for effective management. Regular follow-ups and adjustments to the treatment plan may be necessary to address the evolving needs of the patient as they grow and develop.

Related Information

Description

  • Congenital malformation of hands
  • Reduced number of fingers or fusion
  • Claw-like appearance with underdeveloped thumb
  • Limited hand functionality and grip strength
  • Associated with other congenital anomalies
  • Multidisciplinary treatment including surgery and therapy

Clinical Information

  • Hypoplasia of central digits
  • Prominent thumb and little finger
  • Possible syndactyly present
  • Deformity of the hands evident
  • Functional limitations reported
  • Associated conditions possible
  • Congenital origin confirmed
  • Family history significant
  • Male predominance noted

Approximate Synonyms

  • Ectrodactyly
  • Split Hand/Foot Malformation (SHFM)
  • Cleft Hand
  • Lobster Claw Deformity
  • Congenital Limb Deformities
  • EEC Syndrome
  • SHFM Syndromes
  • Genetic Mutations TP63

Diagnostic Criteria

  • Deformity of hand appears claw-like
  • Bilateral presentation in Q71.63
  • Limb malformations associated with condition
  • Other skeletal abnormalities present
  • Syndromic associations may be present
  • X-rays assess bone structure of hands
  • Chromosomal analysis for genetic testing
  • Comprehensive medical and family history

Treatment Guidelines

  • Surgical intervention may improve hand function
  • Release surgery separates fused fingers
  • Reconstruction creates more functional hand structure
  • Tendon transfers enhance grip strength
  • Physical therapy improves flexibility and strength
  • Range of motion exercises maintain finger mobility
  • Strengthening exercises target muscle weakness
  • Adaptive techniques compensate for limitations
  • Occupational therapy develops fine motor skills
  • Assistive devices support hand function
  • Environmental modifications facilitate easier access
  • Psychosocial support helps cope with emotional impact

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